Poland Syndrome

Information

This syndrome is named after the British surgeon (Alfred Poland) who first described it and is a rare disease that affects one in every 20 to 30 thousand children and is characterised by unilateral abnormalities affecting the muscles of the chest or an upper limb, usually the right one.

Malformations can affect the pectoralis major muscles, ribs, chest, arms and fingers. To date, the cause of Poland syndrome is unknown, although it is assumed to be a genetic disorder.

durata intervento

Duration

2 hours

Anaesthesia

General

durata intervento

Recovery

5 days

controllo mastoplastica

Follow-up

1 month after stitches removal

The Results

The malformations are such that they inhibit the correct psychophysical development of affected children, to the extent that correct education allows manual activities to be developed even in carriers of the most severe malformations.

Treatment is surgical and makes use of reconstructive plastic surgery techniques involving flaps, surgical grafts and permanent prostheses.

Each case with Poland syndrome must be carefully evaluated in order to choose the most appropriate surgical technique.

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